Search on: NEUROCUTANEOUS SYNDROMES 
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Descriptor English:   Neurocutaneous Syndromes 
Descriptor Spanish:   Síndromes Neurocutáneos 
Descriptor Portuguese:   Síndromes Neurocutâneas 
Synonyms English:   Neurocutaneous Disorder
Neurocutaneous Disorders
Neurocutaneous Syndrome
Neuroectodermal Dysplasia Syndrome
Neuroectodermal Dysplasia Syndromes
Phacomatoses
Phacomatosis
Phakomatoses
Phakomatosis
Syndrome, Neurocutaneous
Syndrome, Neuroectodermal Dysplasia
Syndromes, Neurocutaneous
Syndromes, Neuroectodermal Dysplasia  
Tree Number:   C10.562
C16.131.077.350.712
C16.131.831.350.712
C16.320.850.250.712
C17.800.804.350.712
C17.800.827.250.712
Definition English:   A group of disorders characterized by ectodermal-based malformations and neoplastic growths in the skin, nervous system, and other organs. 
Indexing Annotation English:   for neurocutaneous melanosis, coord with MELANOSIS
History Note English:   2000 
Allowable Qualifiers English:  
BL blood CF cerebrospinal fluid
CI chemically induced CL classification
CO complications CN congenital
DI diagnosis DG diagnostic imaging
DH diet therapy DT drug therapy
EC economics EM embryology
EN enzymology EP epidemiology
EH ethnology ET etiology
GE genetics HI history
IM immunology ME metabolism
MI microbiology MO mortality
NU nursing PS parasitology
PA pathology PP physiopathology
PC prevention & control PX psychology
RT radiotherapy RH rehabilitation
SU surgery TH therapy
UR urine VE veterinary
VI virology  
Record Number:   34313 
Unique Identifier:   D020752 

Occurrence in VHL:
 

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